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Ataxia

Many of us don’t think about balance until something feels off. Walking across a room, picking up a cup or speaking clearly usually happens automatically. When these simple actions become difficult, it can feel confusing and frightening. 

Ataxia is a condition that affects balance, coordination and muscle control. It can make movements appear shaky, unsteady or poorly coordinated. If you or someone you know has trouble with balance, coordination or steady movement, ataxia may be the reason. 

What is ataxia?

Ataxia is a condition that affects how your body moves. It makes it hard to control balance, coordinate your muscles and move smoothly. Ataxia isn't a single disease. It is a group of conditions that affect different parts of your nervous system, including the brain, nerves and spinal cord.

Your brain and nerves work together to control your movements. When parts of this system don't work properly, your movements can become shaky, unsteady or slow. It may affect your:

  • Eyes
  • Legs
  • Arms
  • Hands
  • Fingers
  • Muscles used for speech

The condition can develop slowly over time or suddenly, depending on its cause. 

How is ataxia different from apraxia?

Ataxia and apraxia may seem similar but they are different conditions. Both affect movement but in different ways. 

While ataxia affects how smoothly and steadily you move, apraxia affects how your brain plans and organizes movement. Your muscles and balance may be normal but your brain has trouble sending the right instructions. 

With apraxia, you might know what you want to do but have a hard time doing it. You may move awkwardly, even if your strength and coordination seem normal. 

What causes ataxia?

Ataxia has different causes. Some are genetic, some are acquired (e.g., brain injury, stroke, tumor, autoimmune conditions), some are due to neurodegenerative illness (e.g., multiple system atrophy) and some are caused by medications, vitamin deficiencies or poisoning (e.g., mercury, long term excessive alcohol consumption).

Ataxia may develop for many different reasons. In general, doctors group causes into three main categories: acquired ataxia, hereditary ataxia and adult-onset or unexplained ataxia.

Acquired ataxia

Acquired ataxia happens when something damages your brain or nervous system after you are born. Symptoms may appear suddenly or gradually. Sometimes, treating the cause can help improve your movement. 

Possible causes include:

  • Brain or nervous system injury: Stroke, head injury and brain tumors
  • Neurodegenerative diseases: Multiple system atrophy (a condition that is like Parkinson’s disease but typically gets worse more quickly)
  • Autoimmune conditions: Paraneoplastic cerebellar degeneration (the body’s overreaction to fighting off a tumor), multiple sclerosis, autoimmune encephalopathy and related conditions
  • Infections: Viral or bacterial infections that affect the brain and post-infectious inflammation
  • Alcohol or toxin exposure: Long-term heavy alcohol consumption and exposure to certain chemicals or heavy metals (e.g., mercury)
  • Medications and treatments: Some chemotherapy drugs and long-term effects of certain seizure or immune medications
  • Nutritional problems: Vitamin E deficiency; vitamin B or copper deficiency can cause severe problems with position sense causing coordination to seem worse (pseudoataxia)

Hereditary ataxia

Hereditary ataxia runs in families. You inherit a gene that affects how your nervous system develops or works. Symptoms often start in childhood, the teen years or early adulthood but some forms appear later in life. 

Common examples include:

  • Friedreich’s ataxia
  • Spinocerebellar ataxia
  • Wilson’s disease
  • Episodic ataxia

Adult-onset ataxia

Sometimes, ataxia occurs without a clear cause. When it starts in adulthood and slowly worsens with no known cause, this should prompt genetic testing.  Only about 40% of cases will have a cause identified, the three most common are:

  • Spinocerebellar ataxia (SCA) type 27b: Often preceded by unexplained cough and attacks of vertigo
  • CANVAS (cerebellar ataxia, neuropathy, vestibular areflexia) syndrome: Often accompanied by chronic cough and dizziness.
  • Hereditary spastic paraplegia type 7 (SPG7): Usually accompanied by tight muscles and leg weakness.   

Common symptoms of ataxia

Ataxia symptoms can look different from person to person. Some may be mild at first and get worse over time. Others can appear without warning. 

Common signs of ataxia include:

  • Trouble walking or frequent falls
  • Poor balance or feeling unsteady
  • Clumsy movements or dropping objects
  • Shaking or tremors
  • Slurred or slow speech
  • Trouble swallowing
  • Difficulty with eye movements
  • Fatigue or weakness

You may notice that everyday tasks require more effort. Buttoning a shirt, writing or using utensils may be more difficult. If these symptoms affect your daily life, see a health care provider.

Types of ataxia

There are three main conditions that can be mistaken for one another: cerebellar ataxia, sensory ataxia (pseudo, or false ataxia) and vestibulopathy. 

Cerebellar ataxia

Your cerebellum is a part of your brain that helps you keep your balance and coordination. If it gets damaged, it can cause a condition called cerebellar ataxia. 

You might notice:

  • Wide, unsteady walking
  • Poor coordination in your arms or hands
  • Difficulty with fine motor skills, such as writing
  • Slurred speech

Sensory ataxia 

Sensory ataxia (also known as pseudoataxia because it resembles cerebellar ataxia) happens when nerves in your spinal cord or peripheral nervous system are damaged. 

You might notice:

  • Trouble knowing where your arms or legs are without looking
  • Stomping your feet to maintain balance
  • Worsening balance when your eyes are closed

Vestibulopathy

Vestibulopathy is not a true ataxia but can resemble it. It happens when your inner ear and ear canals, which have fluid inside, get damaged. These parts help you sense your head movements and help with balance and spatial orientation. 

You might notice:

  • Dizziness or spinning sensations
  • Trouble walking straight
  • Feeling unsteady on uneven surfaces
  • Nausea

How ataxia is diagnosed

Diagnosing ataxia usually begins with a detailed medical history and a complete neurological exam. Your health care provider will ask about your health history, family history and symptoms. They will also perform a physical exam but may need to refer you to a neurologist or movement disorder specialist for the neurological exam. 

Tests to decide the cause of ataxia and related symptoms may include:

  • Imaging tests, such as MRI or CT scans, to look at the brain
  • Blood tests to check for infections, vitamin levels or immune issues
  • Genetic testing is performed if a hereditary condition is suspected
  • Nerve studies and electromyography to assess nerve function

Getting a clear diagnosis may take time but understanding the cause helps guide the best care plan. 

Ataxia treatment options

There is no single cure for ataxia. The treatment plan will depend on the type and cause of ataxia. Some types can be reversed with treatment, while for others the goal is to manage symptoms and help with daily activities. 

For example, vitamin deficiencies can cause ataxia but taking the right supplements might fix it. Infections and autoimmune causes are often treatable. If the ataxia is caused by a neurodegenerative or genetic illness, your provider can help you manage the symptoms. This might include medicines and different types of therapies.

Some genetic forms of ataxia (e.g., Freidreich’s ataxia) now have FDA approved treatments.  For several others, including spinocerebellar ataxias, clinical trials are underway evaluating promising treatments.   

Medication

While no medication cures ataxia, some medicines help manage accompanying symptoms such as erratic blood pressure, muscle stiffness or seizures.

Physical therapy

Physical therapy can help you:

  • Improve balance and coordination
  • Strengthen muscles
  • Learn safer ways to move and walk

Occupational therapy

Occupational therapy focuses on daily activities. You may learn new ways to:

  • Dress
  • Eat
  • Write
  • Use assistive tools

Speech therapy

If ataxia affects your speech or swallowing, speech therapy can help. A speech therapist can work with you to:

  • Speak more clearly
  • Improve swallowing safety
  • Reduce the risk of choking

Living with ataxia

Support makes a difference for those living with ataxia. Building a care team, staying active and making small adjustments at home can help you stay safe and engaged.

  • Use adaptive devices to help you move around and do daily tasks
  • Make your home safer by removing tripping hazards
  • Take breaks when you feel tired
  • Ask for help when you need it

Because genetic ataxias can be passed along to your children, a positive genetic test should prompt family planning conversations with a qualified neurologist and/or genetic counselor.

Counseling and support groups

Living with ataxia can be hard. It affects you physically and emotionally. For some people, it may lead to depression or anxiety. Talking to a licensed therapist or joining a support group for ataxia can help you feel supported and encouraged. 

When to see a health care provider

You should see a health care provider if you notice:

  • Ongoing balance problems
  • Frequent falls
  • Slurred speech
  • Troubling using your hands
  • Sudden changes in coordination

If symptoms appear suddenly, seek medical care right away. Sudden ataxia can be a medical emergency. 

Frequently asked questions about ataxia 

Is ataxia a disease? 

Ataxia is not a single disease. It is a group of conditions that affect coordination and balance. 

Can ataxia be treated? 

Treatment depends on the cause. Some types improve when the underlying problem is treated, while others focus on managing symptoms. 

Is ataxia genetic? 

Some forms of ataxia are inherited. Genetic testing may be recommended if doctors suspect a hereditary condition. 

Is ataxia progressive? 

Some types worsen over time, especially hereditary or neurodegenerative forms. Others may remain stable or improve if the cause is treated. 

Take the next step

If you or a loved one is experiencing ataxia symptoms, Banner Health can help. Our experts are ready to guide you through diagnosis, treatment and ongoing care.

You deserve answers, support, and compassionate care. Make an appointment today and take the next step toward better balance and quality of life.